Nigerian surgeon removes baby from mother's womb, operates on her tumor & returns her back
When Margaret Boemer went for a routine ultrasound 16 weeks into her pregnancy with her third child, she found out that things were far from routine.
"They saw something on the scan, and the doctor came in and told us that there was something seriously wrong with our baby and that she had a sacrococcygeal teratoma," the Plano, Texas, mom said in an interview shared by Texas Children's Hospital. "And it was very shocking and scary, because we didn't know what that long word meant or what diagnosis that would bring,"
Sacrococcygeal teratoma is a tumor that develops before birth and grows from a baby's coccyx, the tailbone. Found more often in girls than boys, this tumor occurs in one out of every 35,000 births.
"This is the most common tumor we see in a newborn," said Dr. Darrell Cass, co-director of Texas Children's Fetal Center and associate professor of surgery, pediatrics and obstetrics and gynecology at Baylor College Medicine. "Even though it's the most common we see, it's still pretty rare."Booemer had been pregnant with twins, but lost one of the babies before her second trimester so it was a shock at 16 weeks to learn of her daughter's rare birth defect.
"Some of these tumors can be very well-tolerated, so the fetus has it and can get born with it and we can take it out after the baby's born," said Cass. "But about half of the time, they cause problems for the fetus and it's usually causing problems because of a blood flow problem."Cass explained that the tumor is trying to grow by sucking blood flow from the baby, yet the baby is also trying to grow, too "so it becomes a competition. And in some instances, the tumor wins and the heart just can't keep up and the heart goes into failure and the baby dies," he said.
With a large tumor stealing the blood supply, Boemer's fetus was becoming more ill each day, doctors explained to the expectant mother. Something had to be done.
Although other doctors had advised her to terminate the pregnancy, Cass and his team told her about another possibility: fetal surgery. This option, though, would not be an easy road. Even worse, her baby's chances of survival would be grim.
"LynLee didn't have much of a chance," Boemer said. "At 23 weeks, the tumor was shutting her heart down and causing her to go into cardiac failure, so it was a choice of allowing the tumor to take over her body or giving her a chance at life. It was an easy decision for us: We wanted to give her life.She was 23 weeks and 5 days pregnant, when Cass and his partner surgeon, Dr. Oluyinka Olutoye, performed the emergency fetal surgery. By this time, the tumor was nearly larger than the fetus. They operated for about five hours.
"The part on the fetus we do very, very quickly," said Cass. "It's only 20 minutes or so on the actual fetus." Most of the time is spent opening the uterus, which he described as "a big muscle lined with membranes. We don't want the mom's health to be jeopardized," said Cass, who explained they work carefully, both making the incision and sewing it up in order "to make that uterus be as sealed and as water tight as possible."Still, Cass said, the tumor in this case was so large a huge incision was needed to get to it, "so it ended up that the baby was hanging out in the air... Essentially, the fetus is outside, like completely out, all the amniotic fluid falls out, it's actually fairly dramatic," said Cass.
During the surgery, LynLee's heart slowed down to an incredibly low rate.
"It basically stopped," said Cass. He credits the heart specialist, a key member of the team, for giving the right medication and transfusing the right amount of fluid, allowing the surgeons to continue their work. The surgical team removed the bulk of the tumor. When they finished their operation, the surgeons placed LynLee back inside the womb and sewed her mother's uterus shut. It's kind of a miracle you're able to open the uterus like that and seal it all back and the whole thing works," said Cass.Boemer was on bed rest for the remainder of her pregnancy. Despite her pain, she marshaled her strength and made it another 12 weeks to nearly 36 weeks -- full term -- when Lynlee Hope was born for the second time via C-section on June 6. She weighed 5 pounds and 5 ounces.
After she was born, LynLee faced one more ordeal: removing the bits of tumor that surgeons could not reach, which had begun to grow again.
"At eight days old, she had more surgery, and they were able to remove the rest of the tumor," explained Boemer. LynLee recovered in the NICU and weeks later, arrived in her family home. Baby Boemer is still an infant but is doing beautiful," said Cass, remarking that she is perfectly healthy. His one previous surgery of this kind was also a success. "I think she's about 7 now, and she sings karaoke to Taylor swift -- she's completely normal," said Cass.
Source:LIB.
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